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注意事項

G6PD缺乏症是一種遺傳疾病,並且是終身的。目前無法治癒此疾病。最重要的是預防由氧化應激引起的急性溶血。因此,G6PD缺乏症患者應終生採取以下預防措施。

高風險藥物

  • Diaminodiphenyl sulfone (Dapsone)

  • Flutamide (Eulexin)

  • Furazolidone (Furoxone)

  • Isobutyl nitrite

  • Methylene blue

  • Niridazole (Ambilhar)

  • Nitrofurantoin (Furadantin)

  • Phenazopyridine (Pyridium)

  • Primaquine

  • Rasburicase (Elitek)

  • Sulfacetamide

  • Sulfanilamide

  • Sulfapyridine

G6PD缺乏症患者應避免的藥物

中度風險藥物

對於患有G6PD缺乏症的患者(無非球形溶血性貧血),在治療劑量中應謹慎使用的藥物

  • Acetaminophen (Tylenol)

  • Acetylsalicylic acid (aspirin)

  • Antazoline (Antistine)

  • Antipyrine

  • Ascorbic acid (vitamin C): intravenous doses only reported

  • Benzhexol (Artane)

  • Chloramphenicol

  • Chlorguanidine (Proguanil, Paludrine)

  • Chloroquine

  • Colchicine

  • Diphenyldramine (Benadryl)

  • Glyburide (glibenclamide, Diabeta, Glynase)

  • Isoniazid

  • L-Dopa

  • Quinine

  • Streptomycin

  • Sulfacytine

  • Sulfadiazine

  • Sulfaguanidine

  • Sulfamethoxazole (Gantanol)

  • Sulfisoxazole (Gantrisin)

  • Trimethoprim

  • Tripelennamine (Pyribenzamine)

  • Vitamin K

其他避免清單

2. Avoid eating fava or broad beans and their products:

3. Avoid close contact with mothballs (Naphthalene) and naphthalene-containing products.

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