注意事項
G6PD缺乏症是一種遺傳疾病,並且是終身的。目前無法治癒此疾病。最重要的是預防由氧化應激引起的急性溶血。因此,G6PD缺乏症患者應終生採取以下預防措施。
高風險藥物
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Diaminodiphenyl sulfone (Dapsone)
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Flutamide (Eulexin)
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Furazolidone (Furoxone)
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Isobutyl nitrite
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Methylene blue
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Niridazole (Ambilhar)
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Nitrofurantoin (Furadantin)
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Phenazopyridine (Pyridium)
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Primaquine
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Rasburicase (Elitek)
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Sulfacetamide
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Sulfanilamide
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Sulfapyridine
G6PD缺乏症患者應避免的藥物
中度風險藥物
對於患有G6PD缺乏症的患者(無非球形溶血性貧血),在治療劑量中應謹慎使用的藥物
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Acetaminophen (Tylenol)
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Acetylsalicylic acid (aspirin)
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Antazoline (Antistine)
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Antipyrine
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Ascorbic acid (vitamin C): intravenous doses only reported
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Benzhexol (Artane)
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Chloramphenicol
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Chlorguanidine (Proguanil, Paludrine)
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Chloroquine
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Colchicine
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Diphenyldramine (Benadryl)
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Glyburide (glibenclamide, Diabeta, Glynase)
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Isoniazid
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L-Dopa
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Quinine
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Streptomycin
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Sulfacytine
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Sulfadiazine
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Sulfaguanidine
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Sulfamethoxazole (Gantanol)
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Sulfisoxazole (Gantrisin)
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Trimethoprim
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Tripelennamine (Pyribenzamine)
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Vitamin K
其他避免清單


2. Avoid eating fava or broad beans and their products:

3. Avoid close contact with mothballs (Naphthalene) and naphthalene-containing products.